白塞病中的淀粉样变性

Amyloidosis in Behçet's disease.

作者信息

Peces R, Riesgo I, Ortego F, Velasco J, Alvarez Grande J

出版信息

Nephron. 1984;36(2):114-7. doi: 10.1159/000183129.

Abstract

A 36-year-old man with Behçet's disease developed nephrotic syndrome and chronic renal failure. The renal biopsy confirmed renal amyloidosis, and the potassium permanganate staining indicated that the amyloid was of the AA protein type. To our knowledge, this is the first report of Behçet's disease with amyloidosis and chronic renal failure in maintenance hemodialysis.

摘要

一名36岁的白塞病男性患者出现了肾病综合征和慢性肾衰竭。肾活检证实为肾淀粉样变性，高锰酸钾染色显示淀粉样物质为AA蛋白类型。据我们所知，这是首例关于白塞病合并淀粉样变性及慢性肾衰竭并接受维持性血液透析的报道。