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病例报告:急性出血性多灶性血管性脑病

Case report: acute hemorrhagic multifocal angioencephalopathy.

作者信息

Pick P, Horoupian D

出版信息

Clin Neuropathol. 1984 Mar-Apr;3(2):88-91.

PMID:6713756
Abstract

A 53-year-old chronic alcoholic male developed an acute febrile, fulminant fatal encephalopathy which lasted 2.5 weeks. Necropsy showed focal, acute hemorrhagic necrotizing lesions of the diencephalon, cingulate gyrus, and amygdala, apparently due to a vasculopathy involving mainly small veins. The case is unique, but the pathology is somewhat similar to an idiopathic disorder described as subacute diencephalic angioencephalopathy [DeGirolami et al. 1974, Kinney et al. 1980].

摘要

一名53岁的慢性酒精中毒男性患上了一种急性发热性、暴发性致命性脑病,病程持续了2.5周。尸检显示间脑、扣带回和杏仁核有局灶性急性出血性坏死性病变,显然是由于主要累及小静脉的血管病变所致。该病例较为独特,但其病理学表现与一种被描述为亚急性间脑血管性脑病的特发性疾病有些相似[德吉罗拉米等人,1974年;金尼等人,1980年] 。

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Case report: acute hemorrhagic multifocal angioencephalopathy.病例报告:急性出血性多灶性血管性脑病
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