Zak T A
J Pediatr Ophthalmol Strabismus. 1984 Mar-Apr;21(2):69-73. doi: 10.3928/0191-3913-19840301-06.
A case of primary congenital upper eyelid entropion ( PCUEE ) is reviewed. The author proposes a congenital shortness of the levator muscle with anomalous insertion onto the tarsal plate as the etiology, and a new simplified surgical correction is described. The classification of PCUEE as a syndrome with multiple congenital anomalies is supported, and the need for a complete systemic evaluation is stressed. Congenital primary upper eyelid entropion is an exceedingly rare condition. In 1969, Hiles and Wilder reviewed the 13 known cases in the ophthalmic literature, and presented a new case. They suggested the possibility that congenital upper eyelid entropion was part of a syndrome involving multiple systemic anomalies. Surgical correction of the ectropion is usually necessitated by corneal erosion secondary to trichiasis, and a multifarious assortment of surgical procedures has been described. The following is a case report of primary congenital upper eyelid entropion which corroborates the categorization as a syndrome, suggests a pathophysiologic abnormality of the eyelid as the etiology, and describes a new, simplified technique of surgical repair.
本文回顾了一例原发性先天性上睑内翻（PCUEE）病例。作者提出病因是提上睑肌先天性短小且异常插入睑板，并描述了一种新的简化手术矫正方法。支持将PCUEE归类为伴有多种先天性异常的综合征，并强调了进行全面系统评估的必要性。先天性原发性上睑内翻是一种极为罕见的病症。1969年，希尔斯和怀尔德回顾了眼科文献中已知的13例病例，并报告了1例新病例。他们认为先天性上睑内翻可能是涉及多种全身异常的综合征的一部分。倒睫继发角膜糜烂通常需要手术矫正睑外翻，并且已经描述了各种各样的手术方法。以下是一例原发性先天性上睑内翻的病例报告，该报告证实了其作为综合征的分类，提示眼睑的病理生理异常为病因，并描述了一种新的简化手术修复技术。
