Park S C, Siewers R D, Neches W H, Mathews R A, Fricker F J, Beerman L B, Fischer D R, Zuberbuhler J R
J Am Coll Cardiol. 1984 Jul;4(1):136-40. doi: 10.1016/s0735-1097(84)80331-9.
A 2 year old boy with ventricular inversion and normal ventriculoarterial connection is described. Associated cardiac lesions included single atrium, absence of the coronary sinus, bilateral superior venae cavae, absence of the hepatic segment of the inferior vena cava with azygos and hemiazygos continuation, right aortic arch, levocardia and left atrial isomerism. At 5 days of age, the patient underwent a Waterston (aortopulmonary) anastomosis because of suspected pulmonary atresia. The correct diagnosis was established at 2 years of age and the patient had a successful Mustard operation (interatrial baffle procedure) and closure of the Waterston anastomosis. Accurate preoperative diagnosis is difficult in this rare cardiac anomaly and the reported mortality rate is high.
本文描述了一名2岁男性患儿，其心脏存在心室反位但心室动脉连接正常。相关心脏病变包括单心房、冠状窦缺如、双侧上腔静脉、下腔静脉肝段缺如伴奇静脉和半奇静脉延续、右位主动脉弓、左位心及左心房异构。患儿5日龄时，因疑似肺动脉闭锁接受了沃特斯顿（主动脉-肺动脉）吻合术。2岁时确诊，患儿成功接受了马斯塔德手术（房间隔造障术）并关闭了沃特斯顿吻合口。这种罕见的心脏畸形术前准确诊断困难，且报道的死亡率很高。
