[Atrophic macular degeneration in a patient with olivopontocerebellar atrophy].

Description of a man with heredoataxia, presenting with an isolated primary atrophic maculopathy in which the participation of the posterior pole was disclosed by photopic and scotopic ERG irrespective of the localized appearance of this condition. Ophthalmoscopically, the patient's sister showed only fine pigment migrations at the macula, whereas local ERG revealed a macular lesion.