Martini A K, Banniza von Bazan U
Handchir Mikrochir Plast Chir. 1982 Dec;14(4):210-2.
The Freeman-Sheldon syndrome is a rare symptom complex. The hand has flexion contracture and ulnar deviation of the middle finger as well as flexion and adduction contracture of the thumb. The clinical and genetic findings in 11 cases and the results of treatment of six hands are reported. Deformity of the thumb is foremost in contributing to the functional impairment of the hand in determining the mode of treatment. Several different plans of management are available: Z-plasties, muscle transposition, capsulotomies, skin flaps. The treatment should be individualized.
弗里曼-谢尔顿综合征是一种罕见的症状复合体。手部有屈曲挛缩、中指尺偏，以及拇指的屈曲和内收挛缩。报告了11例患者的临床和基因学发现以及6只手的治疗结果。在确定治疗方式时，拇指畸形对手部功能损害的影响最为突出。有几种不同的治疗方案可供选择：Z成形术、肌肉转位、关节囊切开术、皮瓣移植。治疗应个体化。
