常见先天性止血障碍的管理。
Management of common congenital disorders of haemostasis.
作者信息
Ekert H
出版信息
Paediatrician. 1980;9(2):81-8.
PMID:6771736
Abstract
The management of haemophilia, Christmas disease and von Willebrand's syndrome are reviewed. The principal advances in diagnosis are the measurement of procoagulant activity, the ristocetin cofactor and the levels of the protein associated with procoagulant activity by immunologic methods. The mainstay of treatment is replacement of the coagulation factors by partially or highly purified blood products.
摘要
对血友病、克里斯马斯病和血管性血友病综合征的治疗进行了综述。诊断方面的主要进展包括通过免疫方法测定促凝活性、瑞斯托霉素辅因子以及与促凝活性相关的蛋白质水平。治疗的主要方法是用部分纯化或高度纯化的血液制品替代凝血因子。
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Management of common congenital disorders of haemostasis.常见先天性止血障碍的管理。
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