Increase of ornithine transcarbamylase protein in sparse-fur mice with ornithine transcarbamylase deficiency.
作者信息
Briand P, Cathelineau L, Kamoun P, Gigot D, Penninckx M
出版信息
FEBS Lett. 1981 Jul 20;130(1):65-8. doi: 10.1016/0014-5793(81)80666-7.
PMID:6793393
Abstract
摘要
相似文献
1
Increase of ornithine transcarbamylase protein in sparse-fur mice with ornithine transcarbamylase deficiency.鸟氨酸转氨甲酰酶缺乏的稀毛小鼠中鸟氨酸转氨甲酰酶蛋白的增加。
FEBS Lett. 1981 Jul 20;130(1):65-8. doi: 10.1016/0014-5793(81)80666-7.
2
Sparse-fur mutation: a model for some human ornithine transcarbamylase deficiencies.稀疏毛突变：一种人类鸟氨酸转氨甲酰酶缺乏症的模型。
Adv Exp Med Biol. 1982;153:185-94. doi: 10.1007/978-1-4757-6903-6_24.
3
Further evidence for a separate enzymic entity for the synthesis of homocitrulline, distinct from the regular ornithine transcarbamylase.存在一种与常规鸟氨酸转氨甲酰酶不同的、用于合成高瓜氨酸的独立酶实体的进一步证据。
Enzyme. 1984;32(1):26-36. doi: 10.1159/000469447.
4
Expression of ornithine transcarbamylase deficiency in the small intestine and colon of sparse-fur mutant mice.鸟氨酸转氨甲酰酶缺乏症在稀毛突变小鼠小肠和结肠中的表达
J Pediatr Gastroenterol Nutr. 1985 Feb;4(1):118-24. doi: 10.1097/00005176-198502000-00021.
5
Ornithine transcarbamylase deficiencies in human males. Kinetic and immunochemical classification.人类男性中的鸟氨酸转氨甲酰酶缺乏症。动力学和免疫化学分类。
Biochim Biophys Acta. 1982 May 21;704(1):100-6. doi: 10.1016/0167-4838(82)90136-4.
6
Immunoenzymatic studies of ornithine transcarbamylase (OTC) in liver of patients with OTC deficiency by enzyme linked immunosorbent assay (ELISA).采用酶联免疫吸附测定法（ELISA）对鸟氨酸转氨甲酰酶（OTC）缺乏症患者肝脏中的鸟氨酸转氨甲酰酶进行免疫酶学研究。
Tohoku J Exp Med. 1987 May;152(1):15-21. doi: 10.1620/tjem.152.15.
7
Compared expression levels of ornithine transcarbamylase and carbamylphosphate synthetase in liver and small intestine of normal and mutant mice.比较正常小鼠和突变小鼠肝脏及小肠中鸟氨酸转氨甲酰酶和氨甲酰磷酸合成酶的表达水平。
Biochim Biophys Acta. 1988 Sep 7;950(3):321-8. doi: 10.1016/0167-4781(88)90128-5.
8
Immunochemical assay in 16 boys with ornithine transcarbamylase deficiency.
Adv Exp Med Biol. 1982;153:53-62. doi: 10.1007/978-1-4757-6903-6_8.
9
Transient hyperammonemia during aging in ornithine transcarbamylase-deficient, sparse-fur mice.鸟氨酸转氨甲酰酶缺乏、毛稀小鼠衰老过程中的短暂高氨血症
Biochem Int. 1985 Nov;11(5):637-43.
10
The role of hepatic ornithine transcarbamylase deficiency in the orotic aciduria of pregnant mice.肝脏鸟氨酸转氨甲酰酶缺乏在妊娠小鼠乳清酸尿症中的作用。
Eur J Obstet Gynecol Reprod Biol. 1986 Jul;22(3):183-91. doi: 10.1016/0028-2243(86)90065-1.
引用本文的文献
1
Patient selection may affect gene therapy success. Dominant negative effects observed for ornithine transcarbamylase in mouse and human hepatocytes.患者选择可能会影响基因治疗的成功率。在小鼠和人类肝细胞中观察到鸟氨酸转氨甲酰酶的显性负效应。
J Clin Invest. 1996 Feb 1;97(3):826-32. doi: 10.1172/JCI118482.
2
Ornithine transcarbamylase in liver mitochondria.肝脏线粒体中的鸟氨酸转氨甲酰酶。
Mol Cell Biochem. 1982 Nov 26;49(2):97-111. doi: 10.1007/BF00242488.
3
Genetic control of ornithine transcarbamylase induction in chick kidney.
Biochem Genet. 1983 Oct;21(9-10):843-55. doi: 10.1007/BF00483944.
4
Immunological evidence for an ornithine transcarbamylase lesion resulting in the formation of enzyme with smaller protein subunits.鸟氨酸转氨甲酰酶损伤导致形成具有较小蛋白质亚基的酶的免疫学证据。
J Inherit Metab Dis. 1983;6(4):149-52. doi: 10.1007/BF02310869.
5
Correction of mouse ornithine transcarbamylase deficiency by gene transfer into the germ line.通过基因转移到生殖系来纠正小鼠鸟氨酸转氨甲酰酶缺乏症。
Nucleic Acids Res. 1988 Mar 25;16(5):2099-110. doi: 10.1093/nar/16.5.2099.
Zotero 插件