Morville P, Motté J, Gaillard D, Tholon J P, Pennaforte F
Arch Mal Coeur Vaiss. 1981 May;74(5):517-25.
Two cases of supero-inferior heart are reported. Segmental analysis of the first case showed: situs solitus, atrioventricular (left sided loop) and ventriculoarterial discordance, resulting in a corrected transposition with the aorta in L malposition. The second malformation arose on a situs inversus, atrioventricular concordance (left sided loop) and double outlet right ventricle. The right ventricle was on the right and above the left ventricle giving an appearance of paradoxal discordance. The atrioventricular connections determined a plane of cleavage between right and left circulations in the supero-inferior ventricles and an appearance of crossed circulations in the second case. Hypoplasia of the inflow tract, of the right ventricular sinus is almost constant in this type of spatial orientation of the ventricles. The embryological hypoplasias are suggestive of an abnormality in the rotation of the cardiac tube in a frontal plane for the superimposed ventricles and abnormal rotation secondary to ventricular septation in the hearts with crossed circulations. The different classifications proposed in the literature are discussed with respect to these cases.
报告了两例上下型心脏病例。对第一例病例的节段分析显示:心房正位,房室(左侧袢)和心室动脉不一致,导致矫正型大动脉转位,主动脉位于左位异常。第二种畸形发生于心房反位、房室一致(左侧袢)和右心室双出口。右心室位于左心室的右侧且在其上方,呈现出矛盾不一致的外观。房室连接在上下心室中确定了左右循环之间的分裂平面,在第二例中呈现出交叉循环的外观。在这种心室空间取向类型中,流入道、右心室窦发育不全几乎是恒定的。胚胎发育不全提示在叠加心室的额平面中心脏管旋转异常,以及交叉循环心脏中继发于室间隔形成的异常旋转。针对这些病例讨论了文献中提出的不同分类。