Gregg P J, Price B A, Ellis H A, Stevens J
Clin Orthop Relat Res. 1982 Nov-Dec(171):175-9.
A seven-year-old-boy with neurofibromatosis developed pseudarthrosis of the radius. After treatment by external electrical stimulation of the forearm failed, the pseudarthrosis was excised and the proximal and distal ends of the radius were osteotomized. The bone segments were reversed to correct the deformity and to place bone adjacent to the pseudarthrosis in contact with normal bone. This operation has not been described previously for this condition and, as in all previous reports, failed to produce union. Surprisingly, the excised pseudarthrosis showed no histologic evidence of neurofibroma or impaired osteoblastic function. The surrounding soft tissues may play an important role in the establishment and maintenance of the condition.
一名患有神经纤维瘤病的七岁男孩发生了桡骨假关节。在前臂进行外部电刺激治疗失败后,切除了假关节,并对桡骨的近端和远端进行了截骨术。将骨段翻转以纠正畸形,并使假关节附近的骨与正常骨接触。这种手术在此类病症中此前尚未有过描述,并且与之前所有报告一样,未能实现骨愈合。令人惊讶的是,切除的假关节未显示出神经纤维瘤的组织学证据或成骨细胞功能受损。周围软组织可能在该病症的发生和维持中起重要作用。