Kennedy R E
Trans Am Ophthalmol Soc. 1982;80:205-17.
The extremely rare occurrence of sibling brothers with left pulsating exophthalmos has been presented with very similar plain film and CT scan findings. Other patients presented demonstrate the strong familial trend of neurofibromatosis, the multiplicity of lesions, the progression of lesions. Genetic counseling is indicated, together with educating the patient and family as to further neurologic deficits which may develop. On-going evaluation at intervals is indicated. Significant cases should only be approached surgically with the realization of the seriousness of what both the patient and doctor may encounter. Surgery, unfortunately, usually cannot offer much help. An interdisciplinary approach with the surgeon, plastic surgeon, neurosurgeon, and ophthalmologist offers a safer approach.
本文报道了极为罕见的同胞兄弟均出现左侧搏动性眼球突出的病例,其平片和CT扫描结果非常相似。其他已报道的患者显示出神经纤维瘤病明显的家族倾向、病变的多发性以及病变的进展情况。需要进行遗传咨询,并告知患者及其家属可能出现的进一步神经功能缺损。建议定期进行持续评估。对于严重的病例,手术治疗时应充分认识到患者和医生可能面临的风险,不幸的是,手术通常帮助不大。外科医生、整形外科医生、神经外科医生和眼科医生共同采取多学科方法提供了更安全的治疗途径。