青年视交叉蛛网膜炎

Opto-chiasmatic arachnoiditis in the young.

作者信息

Iraci G, Gerosa M A, Tomazzoli L, Pardatscher K, Fiore D L, Secchi A G, Tormene A P, Javicoli R, Giordano R, Olivi A

出版信息

Childs Brain. 1983;10(1):48-66. doi: 10.1159/000120098.

DOI:10.1159/000120098

Abstract

14 young patients, operated upon for opto-chiasmatic arachnoiditis by craniotomy are presented. 2 main etiopathogenetic forms (and their respective clinical equivalents) of the disease could be recognized. Only 1 postoperative death occurred, in a patient with a dominant clinical picture of intracranial hypertension. Results of surgery (craniotomy and lysis of adhesions) could be distinguished as positive (functional improvement) in 5 cases, indifferent or negative in the others, with a follow-up duration of up to 23 years. The role of the diagnostic value of the pneumoencephalogram as a basis for surgical indication is discussed: it is felt that this examination, when reported as negative, is not of sufficient value to rule out the diagnosis, which must essentially rely upon clinical data.

摘要

本文报告了14例接受开颅手术治疗视交叉蛛网膜炎的年轻患者。该疾病可识别出2种主要的病因发病形式（及其各自的临床等效形式）。仅1例术后死亡，该患者以颅内高压为主导临床表现。手术结果（开颅和粘连松解）在5例中可区分为阳性（功能改善），其他病例为无差异或阴性，随访时间长达23年。讨论了气脑造影作为手术指征依据的诊断价值：认为该检查结果为阴性时，其价值不足以排除诊断，诊断必须主要依靠临床资料。