Gagliardi C, D'Avino R, Stassano P, Musumeci A, Spampinato N
J Cardiovasc Surg (Torino). 1983 Mar-Apr;24(2):172-4.
A case with marked factor VII deficiency, undergoing open heart surgery for atrial myxoma, is reported. The syndrome was unknown to the patient and only pre-operative routine coagulation studies showed a low prothrombin activity (22%). Further investigations revealed a severe factor VII deficiency. The operation was carried out under factor VII concentrate administration and no bleeding complication occurred.
本文报道了一例患有明显因子 VII 缺乏症的患者,该患者因心房黏液瘤接受心脏直视手术。患者此前并不知晓该综合征,仅术前常规凝血检查显示凝血酶原活性较低(22%)。进一步检查发现严重的因子 VII 缺乏症。手术在给予因子 VII 浓缩物的情况下进行,未发生出血并发症。