[Anatomo-clinical study of the Steele-Richardson-Olszewski presenile syndrome (Description of a case)].

A case of Progressive Supranuclear Palsy (The Steele-Richardson-Olszewski Syndrome) is presented. The chief clinical features are described. The neuropathological investigation confirmed the clinical diagnosis showing neuronal depopulation, gliosis and neurofibrillary degeneration with the characteristic topography in the brain stem, cerebellum and the subthalamic nuclei. They conclude with the hypothesis that sometimes a pregress cranial trauma can have an important role in the onset of this disease.