Kwak R, Kadoya S
J Neurosurg. 1983 Jul;59(1):166-71. doi: 10.3171/jns.1983.59.1.0166.
Two cases of moyamoya disease associated with persistent primitive trigeminal artery (PTA) are reported. The first patient was a 44-year-old man who experienced a sudden severe headache brought about by an intracerebral hematoma in the left temporoparietal lobe. Four-vessel study showed a right-sided PTA and moyamoya disease. The second patient was a 56-year-old woman with similar symptoms and a hematoma in the right temporoparietal lobe. Four-vessel study showed a left-sided PTA and moyamoya disease. Among the 212 PTA cases reported in the literature, none has been associated with moyamoya disease. Moreover, there are no cases of moyamoya disease among the 119 cases of persistent primitive hypoglossal artery (PHA), which is thought to be a vascular anomaly fundamentally similar to PTA. None of the 907 cases of moyamoya disease reported in Japan has been associated with either PTA or PHA. Nonetheless, the embryonic stage when PTA or PHA normally disappears partially overlaps that period when moyamoya-like vascular anomalies have been thought to arise. The possible developmental relationship between these two varieties of vascular abnormality is discussed.
报告了两例伴有持续性原始三叉动脉（PTA）的烟雾病病例。首例患者为一名44岁男性，因左颞顶叶脑内血肿而突发剧烈头痛。四血管造影显示右侧PTA及烟雾病。第二例患者是一名56岁女性，有类似症状，右侧颞顶叶有血肿。四血管造影显示左侧PTA及烟雾病。在文献报道的212例PTA病例中，无例与烟雾病相关。此外，在119例持续性原始舌下动脉（PHA）病例中也无烟雾病病例，PHA被认为是一种与PTA基本相似的血管异常。在日本报告的907例烟雾病病例中，无例与PTA或PHA相关。尽管如此，PTA或PHA正常消失的胚胎期与烟雾病样血管异常被认为出现的时期部分重叠。本文讨论了这两种血管异常之间可能的发育关系。
