Habeck J O, Rockel A
Zentralbl Allg Pathol. 1983;127(5-6):333-7.
A case of embryonal sarcoma of the lung in a 3-year-old boy is reported. The tumour consisted exclusively of immature mesenchymal structures. Lipoblastic, rhabdomyoblastic, and fibroblastic components can be demonstrated. Epithelial tumour structure are absent. The differential diagnosis to the pulmoblastoma is discussed. The child died after 11 months despite of intensive surgical, radiological, and cytostatic therapy by an extensive local tumour recurrence and metastases within the other lung and the choroid plexus of the brain.
报告了一名3岁男孩的肺胚胎性肉瘤病例。肿瘤仅由未成熟的间充质结构组成。可显示出脂肪母细胞、横纹肌母细胞和成纤维细胞成分。不存在上皮性肿瘤结构。讨论了与肺母细胞瘤的鉴别诊断。尽管进行了强化的手术、放射和细胞抑制治疗,但该患儿在11个月后死亡,原因是肿瘤在局部广泛复发,并转移至对侧肺和脑脉络丛。