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Polyneuropathy in progressive external ophthalmoplegia.

作者信息

Gemignani F, Juvarra G, Marbini A, Calzetti S, Bragaglia M M, Govoni E

出版信息

Eur Neurol. 1982;21(3):181-8. doi: 10.1159/000115478.

DOI:10.1159/000115478
PMID:6889507
Abstract

A case of progressive external ophthalmoplegia (PEO) in association with peripheral neuropathy and other neural and visceral manifestations is reported. Pathological studies of the sural nerve demonstrated loss of large myelinated fibers, segmental demyelination with remyelination, and excess of zebra bodies in the Schwann cells on electron microscopy. Peripheral neuropathy in the course of PEO is regarded as a further although rare aspect of a multisystem disease.

摘要

相似文献

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Polyneuropathy in progressive external ophthalmoplegia.
Eur Neurol. 1982;21(3):181-8. doi: 10.1159/000115478.
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