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重叠性骨髓增殖性疾病中的红细胞增多症和显著白细胞增多症。

Erythrocytosis and marked leukocytosis in overlapping myeloproliferative diseases.

作者信息

Shenkenberg T D, Waddell C C, Rice L

出版信息

South Med J. 1982 Jul;75(7):868-9. doi: 10.1097/00007611-198207000-00027.

DOI:10.1097/00007611-198207000-00027
PMID:6953606
Abstract

We describe two patients who had similar features of erythrocytosis and marked leukocytosis but who were subsequently classified as having chronic myelogenous leukemia and polycythemia vera, respectively, using leukocyte alkaline phosphatase scores and cytogenetic studies to detect the Philadelphia chromosome. The patient diagnosed as having polycythemia vera had a leukocyte count of 164,000/cu mm, which remained at similar levels when the patient was not in remission. We believe this is the first well documented case of PV with a leukocyte count above 150,000/cu mm.

摘要

我们描述了两名患者,他们具有相似的红细胞增多症和明显的白细胞增多症特征,但随后分别被归类为患有慢性粒细胞白血病和真性红细胞增多症,这是通过白细胞碱性磷酸酶评分和细胞遗传学研究来检测费城染色体得出的。被诊断为真性红细胞增多症的患者白细胞计数为164,000/立方毫米,在患者未缓解时该计数维持在相似水平。我们认为这是第一例有充分记录的白细胞计数高于150,000/立方毫米的真性红细胞增多症病例。

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