Harada T, Sando I, Stool S E, Myers E N
Arch Otolaryngol. 1980 May;106(5):275-9. doi: 10.1001/archotol.1980.00790290027010.
A histopathologic study of the temporal bones from a 7-year-old girl with Fanconi's anemia syndrome demonstrated (1) hemorrhage in the submucosal layer and the cavity of the middle ear and mastoid, massive in the right ear; (2) hypocellularity of the bone marrow; (3) minor but multiple anomalies of the middle ear; and (4) hypodevelopment of the hook portion of the cochlea and reduced overall length of the cochlear duct. The histopathologic features of these temporal bones appears to suggest that congenital anomalies of the inner ear, as well as those of the external and middle ears, would be possible causes of the deafness that accompanies Fanconi's anemia syndrome.
对一名患有范可尼贫血综合征的7岁女孩的颞骨进行的组织病理学研究显示：（1）中耳和乳突黏膜下层及腔内出血，右侧耳内出血量大；（2）骨髓细胞减少；（3）中耳有轻微但多处异常；（4）耳蜗钩部发育不全，耳蜗管总长度缩短。这些颞骨的组织病理学特征似乎表明，内耳以及外耳和中耳的先天性异常可能是范可尼贫血综合征所伴发耳聋的原因。
