Saito H, Kishimoto S, Furuta M
Ann Otol Rhinol Laryngol. 1981 Jan-Feb;90(1 Pt 1):80-4. doi: 10.1177/000348948109000121.
Temporal bone findings in a case of Möbius syndrome are presented. The most striking pathological feature of the case is that the facial nerves ended in the horizontal segment in the temporal bones on both sides. This finding gives direct evidence that the site of nerve lesion in Möbius syndrome is in the peripheral nerve. Despite the disappearance of facial nerve in the horizontal segment, a neural element reappeared in the vertical segment of the fallopian canal, and moreover, the chorda tympani was found to cross the tympanic cavity in the normal position. This finding suggests that fibers of the chorda tympani sometimes take an alternative pathway via Arnold's nerve.
本文报告了一例莫比乌斯综合征患者的颞骨检查结果。该病例最显著的病理特征是双侧颞骨内面神经均终止于水平段。这一发现直接证明了莫比乌斯综合征的神经病变部位在外周神经。尽管水平段面神经消失，但在面神经管垂直段出现了神经成分，此外，还发现鼓索在正常位置穿过鼓室。这一发现提示鼓索纤维有时会通过阿诺德神经走行替代路径。
