Nath P H, Castaneda-Zuniga W, Zollikofer C, Delany D J, Fulton R E, Amplatz K, Edwards J E
AJR Am J Roentgenol. 1981 Oct;137(4):683-8. doi: 10.2214/ajr.137.4.683.
Eight patients with isolation of a subclavian artery are described. Isolation of subclavian artery is defined as a loss of continuity between the subclavian artery and aorta but with persistent connection to the homolateral pulmonary artery through a ductus arteriosus. The connecting ductus arteriosus may or may not be patent. As the pulmonary vascular resistance is usually lower than the systemic resistance, the isolated subclavian artery is perfused by subclavian steal, and if the connecting ductus arteriosus is patent, flow occurs from the subclavian artery into the pulmonary artery. In this material and in all reported cases, isolation of subclavian artery has always been associated with other anomalies of the aortic arch, such as right aortic arch or bilateral ductus. Its frequent association with intracardiac defects, usually the tetralogy of Fallot, makes its recognition clinically important. Thoracic aortography with delayed filming is the only procedure that allows consistent diagnosis of this rare anomaly during life.
本文描述了8例锁骨下动脉离断的患者。锁骨下动脉离断定义为锁骨下动脉与主动脉之间连续性中断,但通过动脉导管与同侧肺动脉持续相连。连接的动脉导管可能通畅,也可能不通畅。由于肺血管阻力通常低于体循环阻力,离断的锁骨下动脉通过锁骨下动脉盗血获得灌注,若连接的动脉导管通畅,则血流从锁骨下动脉流入肺动脉。在本病例资料以及所有已报道的病例中,锁骨下动脉离断总是与主动脉弓的其他异常相关,如右位主动脉弓或双侧动脉导管。它常与心内缺损相关,通常是法洛四联症,这使得其在临床上的识别具有重要意义。延迟摄片的胸部主动脉造影是唯一能在患者生前对这种罕见异常进行可靠诊断的检查方法。