Rice G P, Paty D W, Ball M J, Tatham R, Kertesz A
Can J Neurol Sci. 1980 Aug;7(3):171-6. doi: 10.1017/s0317167100023155.
Seven members of a family succumbed to prolonged dementing illnesses. In two, those dementia lasted 10 years, spongiform encephalopathy was found at autopsy. This duration of illness has not been a feature in other instances of familial Creutzfeldt-Jakob disease.
一个家族的七名成员死于长期的痴呆症。其中两人的痴呆症持续了10年,尸检时发现有海绵状脑病。这种病程在家族性克雅氏病的其他病例中并非特征性表现。