长期海绵状脑病：一项家族研究。
Spongiform encephalopathy of long duration: a family study.
作者信息
Rice G P, Paty D W, Ball M J, Tatham R, Kertesz A
出版信息
Can J Neurol Sci. 1980 Aug;7(3):171-6. doi: 10.1017/s0317167100023155.
PMID:7004610
Abstract
Seven members of a family succumbed to prolonged dementing illnesses. In two, those dementia lasted 10 years, spongiform encephalopathy was found at autopsy. This duration of illness has not been a feature in other instances of familial Creutzfeldt-Jakob disease.
摘要
一个家族的七名成员死于长期的痴呆症。其中两人的痴呆症持续了10年，尸检时发现有海绵状脑病。这种病程在家族性克雅氏病的其他病例中并非特征性表现。
相似文献
1
Spongiform encephalopathy of long duration: a family study.长期海绵状脑病：一项家族研究。
Can J Neurol Sci. 1980 Aug;7(3):171-6. doi: 10.1017/s0317167100023155.
2
Familial cerebral amyloidosis and spongiform encephalopathy.家族性脑淀粉样变性和海绵状脑病。
J Neurol Neurosurg Psychiatry. 1982 Jan;45(1):37-45. doi: 10.1136/jnnp.45.1.37.
3
Transmission of spongiform encephalopathy from a familial Creutzfeldt-Jakob disease patient of Jewish Libyan origin carrying the PRNP codon 200 mutation.一名携带PRNP密码子200突变的利比亚犹太裔家族性克雅氏病患者的海绵状脑病传播情况。
Neurology. 1992 Jun;42(6):1249-50. doi: 10.1212/wnl.42.6.1249-a.
4
Features of Creutzfeldt-Jakob disease in brains of patients with familial dementia of Alzheimer type.家族性阿尔茨海默型痴呆患者大脑中克雅氏病的特征。
Can J Neurol Sci. 1980 Feb;7(1):51-7.
5
Rapidly progressive dementia caused by spongiform encephalopathy.由海绵状脑病引起的快速进展性痴呆。
West J Med. 1988 Mar;148(3):313-9.
6
Prolonged, progressive dementia with spongiform encephalopathy: a variant of Creutzfeldt-Jakob disease?
Neuroepidemiology. 1988;7(2):56-65. doi: 10.1159/000110137.
7
Familial neurological disease associated with spongiform encephalopathy.与海绵状脑病相关的家族性神经疾病。
Arch Neurol. 1976 Apr;33(4):252-9. doi: 10.1001/archneur.1976.00500040036005.
8
Supranuclear gaze palsy in familial Creutzfeldt-Jakob disease.家族性克雅氏病中的核上性凝视麻痹
Arch Neurol. 1983 Oct;40(10):618-22. doi: 10.1001/archneur.1983.04050090054008.
9
Syndromes of amyotrophic lateral sclerosis and dementia: relation to transmissible Creutzfeldt-Jakob disease.肌萎缩侧索硬化症与痴呆综合征：与可传播性克雅氏病的关系。
Ann Neurol. 1983 Jul;14(1):17-26. doi: 10.1002/ana.410140104.
10
The familial occurrence of Creutzfeldt-Jakob disease and Alzheimer's disease.克雅氏病和阿尔茨海默病的家族性发病情况。
Brain. 1981 Sep;104(3):535-58. doi: 10.1093/brain/104.3.535.
Zotero 插件