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Novel tritium release assays for isovaleryl-CoA and butyryl-CoA dehydrogenases.

作者信息

Rhead W J, Hall C L, Tanaka K

出版信息

J Biol Chem. 1981 Feb 25;256(4):1616-24.

PMID:7007368
Abstract
摘要

相似文献

1
Novel tritium release assays for isovaleryl-CoA and butyryl-CoA dehydrogenases.用于异戊酰辅酶A和丁酰辅酶A脱氢酶的新型氚释放测定法。
J Biol Chem. 1981 Feb 25;256(4):1616-24.
2
Isovaleryl-CoA dehydrogenase: demonstration in rat liver mitochondria by ion exchange chromatography and isoelectric focusing.异戊酰辅酶A脱氢酶:通过离子交换色谱法和等电聚焦法在大鼠肝脏线粒体中的展示。
Proc Natl Acad Sci U S A. 1980 May;77(5):2646-50. doi: 10.1073/pnas.77.5.2646.
3
Isovaleryl-CoA dehydrogenase from rat liver.大鼠肝脏异戊酰辅酶A脱氢酶
Methods Enzymol. 1988;166:374-89. doi: 10.1016/s0076-6879(88)66049-6.
4
Purification and properties of short-chain acyl-CoA, medium-chain acyl-CoA, and isovaleryl-CoA dehydrogenases from human liver.人肝脏中短链酰基辅酶A、中链酰基辅酶A和异戊酰辅酶A脱氢酶的纯化及性质
Adv Neurol. 1988;48:221-30.
5
Identification of Caenorhabditis elegans isovaleryl-CoA dehydrogenase and structural comparison with other acyl-CoA dehydrogenases.秀丽隐杆线虫异戊酰辅酶A脱氢酶的鉴定及其与其他酰基辅酶A脱氢酶的结构比较。
Mol Genet Metab. 2001 Jun;73(2):126-37. doi: 10.1006/mgme.2001.3183.
6
Purification and properties of short chain acyl-CoA, medium chain acyl-CoA, and isovaleryl-CoA dehydrogenases from human liver.人肝脏中短链酰基辅酶A、中链酰基辅酶A和异戊酰辅酶A脱氢酶的纯化及性质
J Biol Chem. 1987 Jun 15;262(17):7982-9.
7
Inhibition in vitro of acyl-CoA dehydrogenases by 2-mercaptoacetate in rat liver mitochondria.2-巯基乙酸对大鼠肝线粒体中酰基辅酶A脱氢酶的体外抑制作用。
Biochem J. 1983 Dec 1;215(3):457-64. doi: 10.1042/bj2150457.
8
Molecular basis of isovaleric acidemia and the study of the acyl-CoA dehydrogenase family.异戊酸血症的分子基础及酰基辅酶A脱氢酶家族的研究
Adv Neurol. 1988;48:107-31.
9
Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.使用改良的氚释放测定法检测异戊酸血症成纤维细胞中的异戊酰辅酶A脱氢酶活性。
Pediatr Res. 1986 Jan;20(1):59-61. doi: 10.1203/00006450-198601000-00017.
10
Catalytic defect of medium-chain acyl-coenzyme A dehydrogenase deficiency. Lack of both cofactor responsiveness and biochemical heterogeneity in eight patients.中链酰基辅酶A脱氢酶缺乏症的催化缺陷。八例患者缺乏辅因子反应性和生化异质性。
J Clin Invest. 1985 Sep;76(3):963-9. doi: 10.1172/JCI112096.

引用本文的文献

1
Conversion of dihydroceramide into ceramide: involvement of a desaturase.二氢神经酰胺向神经酰胺的转化:一种去饱和酶的作用
Biochem J. 1997 Oct 1;327 ( Pt 1)(Pt 1):125-32. doi: 10.1042/bj3270125.
2
Accumulation of phytanic acid alpha-oxidation intermediates in Zellweger fibroblasts.植烷酸α-氧化中间体在齐-韦二氏成纤维细胞中的积累。
J Inherit Metab Dis. 1993;16(3):591-4. doi: 10.1007/BF00711690.
3
Fatty acyl-CoA dehydrogenase deficiency: enzyme measurement and studies on alternative metabolism.
J Inherit Metab Dis. 1984;7 Suppl 1:28-32. doi: 10.1007/BF03047370.
4
Specific glutaryl-CoA dehydrogenating activity is deficient in cultured fibroblasts from glutaric aciduria patients.戊二酸尿症患者培养的成纤维细胞中特定的戊二酰辅酶A脱氢酶活性缺乏。
J Clin Invest. 1984 Mar;73(3):778-84. doi: 10.1172/JCI111271.
5
Catalytic defect of medium-chain acyl-coenzyme A dehydrogenase deficiency. Lack of both cofactor responsiveness and biochemical heterogeneity in eight patients.中链酰基辅酶A脱氢酶缺乏症的催化缺陷。八例患者缺乏辅因子反应性和生化异质性。
J Clin Invest. 1985 Sep;76(3):963-9. doi: 10.1172/JCI112096.
6
The multiple acyl-coenzyme A dehydrogenation disorders, glutaric aciduria type II and ethylmalonic-adipic aciduria. Mitochondrial fatty acid oxidation, acyl-coenzyme A dehydrogenase, and electron transfer flavoprotein activities in fibroblasts.多种酰基辅酶A脱氢酶缺乏症,即II型戊二酸尿症和乙基丙二酸-己二酸尿症。成纤维细胞中的线粒体脂肪酸氧化、酰基辅酶A脱氢酶及电子传递黄素蛋白活性。
J Clin Invest. 1986 Jul;78(1):205-13. doi: 10.1172/JCI112553.
7
Short-chain acyl-coenzyme A dehydrogenase deficiency. Clinical and biochemical studies in two patients.短链酰基辅酶A脱氢酶缺乏症。两名患者的临床和生化研究。
J Clin Invest. 1987 May;79(5):1303-9. doi: 10.1172/JCI112953.
8
The inborn errors of mitochondrial fatty acid oxidation.线粒体脂肪酸氧化的先天性代谢缺陷。
J Inherit Metab Dis. 1987;10 Suppl 1:159-200. doi: 10.1007/BF01812855.
9
Mechanism of hypoglycaemic action of methylenecyclopropylglycine.亚甲基环丙基甘氨酸的降血糖作用机制。
Biochem J. 1989 May 1;259(3):921-4. doi: 10.1042/bj2590921.