Hofmann P, Döhring S, Schumpe G, Lackner K, Brackmann H H
Z Orthop Ihre Grenzgeb. 1982 Apr;120(2):125-33. doi: 10.1055/s-2008-1051590.
A review of the literature was made with special interest in morphology, pathogenesis and treatment of hemophilic pseudotumors. 110 reports of hemophilic pseudotumors were evaluated and compared with 25 own cases. The separation according to the inflicted site and the primarily involved anatomical structure revealed three types of hemophilic pseudotumors: 1. Intramuscular hematomas which enter secondarily into the periosteum. a) In the diaphyses of long tubular bones (femur 49, lower leg 14, humerus 4, forearm 2). b) In the iliac bone (37). 2. Intraspongious cysts in short cancellous bones (calcaneus 14, talus 5, scapula 3). 3. Direct subperiostal hematomas in the phalanges and metacarpals in the hand (thumb 5, finger 1, metacarpal 1). Concerning treatment, there is to state, that in general a conservative approach (substitution of the missing clotting factor and immobilization) is promising. The operative indications are demonstrated and determined, using case reports.
对文献进行了回顾，特别关注血友病性假肿瘤的形态学、发病机制和治疗。评估了110例血友病性假肿瘤的报告，并与25例自身病例进行了比较。根据受累部位和主要累及的解剖结构进行分类，发现血友病性假肿瘤有三种类型：1. 继发于骨膜的肌内血肿。a) 长管状骨干（股骨49例，小腿14例，肱骨4例，前臂2例）。b) 髂骨（37例）。2. 短松质骨内的海绵状囊肿（跟骨14例，距骨5例，肩胛骨3例）。3. 手部指骨和掌骨的直接骨膜下血肿（拇指5例，手指1例，掌骨1例）。关于治疗，需要指出的是，一般来说，保守治疗方法（补充缺失的凝血因子和固定）是有前景的。通过病例报告展示并确定了手术指征。
