表现为腹部肿块的局限性先天性肝纤维化。
Localized congenital hepatic fibrosis presenting as an abdominal mass.
作者信息
Hausner R J, Alexander R W
出版信息
Hum Pathol. 1978 Jul;9(4):473-6. doi: 10.1016/s0046-8177(78)80033-1.
PMID:711226
Abstract
A six month old male with a liver mass localized to the right lobe that had the histological features of congenital hepatic fibrosis is presented. The mass was resected and the patient was asymptomatic 10 months after surgery. This case serves to further broaden the range of lesions with the histological features of congenital hepatic fibrosis; only one other example of localized congenital hepatic fibrosis has been previously reported.
摘要
本文报告了一名6个月大的男性患儿，其肝脏肿块局限于右叶，具有先天性肝纤维化的组织学特征。该肿块已被切除，术后10个月患者无症状。该病例进一步拓宽了具有先天性肝纤维化组织学特征的病变范围；此前仅报道过另一例局限性先天性肝纤维化病例。
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