Musiek F E, Weider D J, Mueller R J
Arch Otolaryngol. 1982 Sep;108(9):595-9. doi: 10.1001/archotol.1982.00790570061015.
An audiologic study of a 54-year-old patient with Charcot-Marie-Tooth disease whose initial symptom was hearing difficulty is presented. While findings from basic audiologic tests were not consistent with the degree of auditory difficulty reported by the patient, special testing did indicate a notable deficit. Although the auditory periphery was probably mildly involved, it seemed that the major auditory deficit was central.
本文介绍了一名54岁患有夏科-马里-图思病(Charcot-Marie-Tooth disease)患者的听力学研究,该患者的初始症状为听力困难。虽然基本听力学测试结果与患者报告的听觉困难程度不一致,但特殊测试确实显示出明显的缺陷。尽管听觉外周可能轻度受累,但主要的听觉缺陷似乎是中枢性的。