Kanamaru R, Gondo M, Hirahara K, Hamada H, Mihara T, Asakura T
No Shinkei Geka. 1982 Jul;10(7):731-6.
The authors reported a case of giant chondromyxoid fibroma of the right anterior cranial fossa, arising from the right orbital lamina of frontal bone. A fifteen-year-old boy was admitted because of a recent history of the right exophthalmus and headache. Neurological examination was essentially negative except papilledema in the both optic fundi and the right olfactory disturbance. Skull plain x-ray films showed the bony destruction of the right supraorbital bone and the some of abnormal calcification in the right anterior cranial fossa. CT scan showed cystic low density spots surrounded by irregular ring-like high density areas in the right anterior cranial fossa. Operation was performed on two stages and the tumor was removed totally. The tumor was arising from the orbital lamina of the frontal bone. The size of resected tumor was 7x5x4 cm. The pathological examination confirmed the diagnosis of chondromyxoid fibroma. Postoperatively, the patient is fully schooling without any disturbance 2 years and 7 months after the discharge. In Japan, two cases of intracranial chondromyxoid fibroma have been reported in literature. The authors discussed the histology of chondromyxoid fibroma and the genesis of the membraneous bone origin of the intracranial chondromatous tumor.
作者报告了一例起源于额骨右眶板的右前颅窝巨大软骨黏液样纤维瘤病例。一名15岁男孩因近期出现右眼球突出和头痛入院。神经系统检查基本正常，仅双侧视乳头水肿和右侧嗅觉障碍。头颅平片显示右眶上骨骨质破坏及右前颅窝一些异常钙化。CT扫描显示右前颅窝有囊性低密度区，周围有不规则环状高密度区。手术分两期进行，肿瘤被完全切除。肿瘤起源于额骨眶板。切除肿瘤大小为7×5×4cm。病理检查确诊为软骨黏液样纤维瘤。术后，患者出院2年7个月后已完全恢复上学，无任何不适。在日本，文献中已报道过两例颅内软骨黏液样纤维瘤病例。作者讨论了软骨黏液样纤维瘤的组织学以及颅内软骨瘤膜性骨起源的发生机制。
