Tejani A, Dobias B, Varma P
Obstet Gynecol. 1978 Oct;52(4):483-5.
An omphalocele is a congenital defect of the abdominal wall, through which intestines and other intraabdominal organs protrude outside the abdominal cavity. The defect in the abdominal wall is covered by a translucent sac composed of peritoneum internally and amniotic membrane externally, through which the viscera can be seen. Such an anomaly is obvious and easily recognized at birth when the defect in the abdominal wall is large, but a small defect, also designated as umbilical cord hernia, is often unnoticed and may, when the cord is clamped, result in an iatrogenic laceration of the gut. We report such an encounter to alert the physician and suggest a method to prevent the iatrogenic misadventure. A careful follow-up of the child, including developmental evaluation, is presented and compared with her healthy twin. A review of the relevant literature shows that the anomaly is not rare and that there is often a delay of several days in establishing the correct diagnosis, leading to a fatal outcome in some cases.
脐膨出是一种腹壁先天性缺陷，肠管及其他腹腔内器官经由此缺陷突出于腹腔外。腹壁缺损被一层半透明囊所覆盖，该囊内层为腹膜，外层为羊膜，透过此囊可看到内脏。当腹壁缺损较大时，这种异常在出生时很明显且易于识别，但较小的缺损，也称为脐带疝，常未被注意到，并且在结扎脐带时，可能导致肠道医源性撕裂。我们报告这样一例病例以提醒医生，并提出一种预防医源性不良事件的方法。本文展示了对该患儿进行的包括发育评估在内的仔细随访情况，并与她健康的双胞胎进行了比较。相关文献回顾表明，这种异常并不罕见，而且在确立正确诊断方面常常会延迟数天，在某些情况下会导致致命后果。
