Peiker G, Böhm W, Carol W
Zentralbl Gynakol. 1978;100(17):1126-30.
Report on a classical Laurence-Moon-Bardet-Biedl-syndrome (LMBB-Syndrome). After a 9 (to 10) year-period of irregular bleedings caused by proved monophasic menstrual cycles and Stein-Leventhal-syndrome an endometrial adenocarcinoma arose in the 23 old patient. The possible carcinogenesis by virtue of an extraglandular oestrogen-(oestron-) production is discussed. The frequently observed nephropathy is often a decisive factor in morbidity and letyality of the LMBB-syndrome.
一例典型的劳伦斯-穆恩-巴德-比德尔综合征(LMBB综合征)报告。在一名23岁患者中,由已证实的单相月经周期和斯坦因-莱文塔尔综合征导致的9(至10)年不规则出血后,发生了子宫内膜腺癌。讨论了由于腺体外雌激素(雌酮)产生而可能的致癌机制。经常观察到的肾病往往是LMBB综合征发病率和死亡率的决定性因素。