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弗里德赖希共济失调患者血小板中的活性丙酮酸脱氢酶。

Active pyruvate dehydrogenase in platelets from Friedreich's ataxia patients.

作者信息

Filla A, Butterworth R F, Barbeau A

出版信息

Can J Neurol Sci. 1980 Nov;7(4):417-9. doi: 10.1017/s0317167100022988.

Abstract

Pyruvate dehydrogenase (PDH) activity was measured in platelets from 10 patients with Friedreich's ataxia, and 10 age-matched healthy control subjects. Both total PDH and active PDH activity were measured. There were no significant differences between the two groups.

摘要

在10例弗里德赖希共济失调患者及10名年龄匹配的健康对照者的血小板中检测了丙酮酸脱氢酶(PDH)活性。同时检测了总PDH活性和活性PDH活性。两组之间无显著差异。

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