Bruneton J N, Drouillard J, Rabin A, Boedec R, Broussin J, Delorme G
J Can Assoc Radiol. 1978 Dec;29(4):252-61.
Two patients with renal angiomyolipomas studied angiographically are reported:--A case of tuberous sclerosis with bilateral multiple lesions, renal, hepatic and adrenal;--An isolated lesion whose preoperative diagnosis allowed the excision of the tumor. A review of the literature from 1965 to 1977 identified 242 cases of which 177 were isolated angiomyolipomas. There were 54 cases associated with tuberous sclerosis and one with von Hippel-Lindau disease. The radiologic and especially the angiographic signs are illustrated, the hemorrhagic risks are stressed, and the diagnostic features of fetal renal hamartoma are described.
本文报告了2例经血管造影研究的肾血管平滑肌脂肪瘤患者:——1例结节性硬化症患者,双侧肾脏、肝脏和肾上腺出现多发病变;——1例孤立性病变,术前诊断明确,得以切除肿瘤。回顾1965年至1977年的文献,共发现242例病例,其中177例为孤立性血管平滑肌脂肪瘤。54例与结节性硬化症相关,1例与冯·希佩尔-林道病相关。文中阐述了放射学表现,尤其是血管造影征象,强调了出血风险,并描述了胎儿肾错构瘤的诊断特征。