Lam W, Danoviz J, Witham D, Wyndham C, Rosen K M
Chest. 1981 Jun;79(6):700-2. doi: 10.1378/chest.79.6.700.
The findings in a 22-year-old man with Ebstein's anomaly of the tricuspid valve, Wolff-Parkinson-White syndrome, and a persistent left superior vena cava are reported. This is the first reported case of this combination of anomalies in which the atrial septum was intact and the left superior vena cava communicated with the left atrium. Uniquely, blood was shunted left to right via the left superior vena cava from the left atrium. Only one previous case of left-to-right shunting via a left superior vena cava (in the absence of mitral valvular disease or cor triatriatum) has been reported (associated with aortic coarctation). Angiograms demonstrated the left atrial connection of the left superior vena cava to be at the entrance of the right superior pulmonary vein into the left atrium. In the absence of demonstrable left-sided heart disease, this anatomic juxtaposition is suggested as a possible explanation for the direction of shunting.
报告了一名22岁男性，患有三尖瓣埃布斯坦畸形、预激综合征和永存左上腔静脉。这是首次报道的这种异常组合病例，其房间隔完整，左上腔静脉与左心房相通。独特的是，血液通过左上腔静脉从左心房向右分流。此前仅报道过一例通过左上腔静脉进行左向右分流的病例（无二尖瓣疾病或三房心）（与主动脉缩窄有关）。血管造影显示左上腔静脉与左心房的连接位于右上肺静脉进入左心房的入口处。在没有明显左侧心脏病的情况下，这种解剖位置关系被认为是分流方向的一种可能解释。
