Riemann J F, Schmidt H
Endoscopy. 1981 Mar;13(2):60-3. doi: 10.1055/s-2007-1021648.
Intestinal lymphangiectasia may present as a primary congenital disorder as well as a secondary form due to numerous underlying diseases. Endoscopically, whitish swollen tips of the villi are fairly characteristic; histologically, dilatation of the lymphatics can be demonstrated. By means of electron microscopy dilated intercellular spaces with aggregation of protein precipitations as well as ectatic lymph vessels with abnormal structure are found. Possible relations to the pathomechanism are discussed.
肠淋巴管扩张症可表现为原发性先天性疾病，也可作为继发形式由多种潜在疾病引起。在内镜检查中，绒毛顶端发白肿胀颇具特征；在组织学上，可显示淋巴管扩张。通过电子显微镜检查，发现细胞间隙扩张伴有蛋白质沉淀聚集，以及结构异常的扩张淋巴管。文中讨论了其与发病机制的可能关系。
