Hintner H, Tappeiner G, Egg D, Wolff K
Hautarzt. 1981 Feb;32(2):75-9.
Fasciitis with eosinophilia (also Shulman's disease or eosinophilic fasciitis) is characterized by an inflammatory thickening of the fascia, eosinophilia and hypergammaglobulinemia. It has clinical and histopathological similarities with scleroderma, though evidence for systemic involvement is rarely found. In this report, we describe the clinical and laboratory features of two patients with this disease and their response to treatment and we discuss its relationship to scleroderma and the pseudosclerodermatous syndromes and its prognosis.
嗜酸性筋膜炎(亦称舒尔曼病或嗜酸性粒细胞性筋膜炎)的特征为筋膜炎症性增厚、嗜酸性粒细胞增多及高球蛋白血症。尽管很少发现有系统性受累的证据,但它在临床和组织病理学上与硬皮病相似。在本报告中,我们描述了两名患有此病患者的临床和实验室特征以及他们对治疗的反应,并讨论了其与硬皮病和假性硬皮病综合征的关系及其预后。