Dell P C, Sheppard J E
Clin Orthop Relat Res. 1981 Jun(157):113-8.
Complex syndactyly of the hands and feet is a major deformity seen in children with Apert's syndrome. Also observed in the three patients presented in this paper was severe hallux valgus, which caused significant shoeing difficulties in two patients, for whom surgical correction was necessary. The two operative plans were based on the different underlying osseous abnormalities: (1) removal of the great toe with transposition of the second toe; (2) resection of the second ray with realignment of the great toe. Both procedures were successful from a functional and aesthetic viewpoint. When confronted with a child with Apert's syndrome who is having shoeing difficulty, assessment of the underlying osseous pathology is a mandatory step in the preoperative planning of surgical intervention.
手足复合并指(趾)畸形是Apert综合征患儿常见的主要畸形。本文报道的3例患者还存在严重的拇外翻,其中2例患者穿鞋困难明显,需要手术矫正。两种手术方案基于不同的潜在骨质异常:(1)切除拇趾并将第二趾移位;(2)切除第二跖骨并矫正拇趾。从功能和美观角度来看,两种手术均取得成功。当面对患有Apert综合征且穿鞋困难的患儿时,评估潜在的骨质病理情况是手术干预术前规划中必不可少的一步。