Gibson R, Nihill M R, Mullins C E, Cooley D A, Sandiford F M, McNamara D G
Circulation. 1981 Oct;64(4):857-61. doi: 10.1161/01.cir.64.4.857.
Coronary arterial obstruction associated with congenital aortic valve disease is rare in children. We studied two children with aortic valve disease and symptoms of coronary insufficiency. Cineangiography revealed localized obstruction of the proximal left coronary artery. In one patient, a membrane-like structure partially covered the left sinus of Valsalva, almost isolating the ostium of the left coronary artery; the other patient had severe stenosis of the proximal left coronary artery and a congenitally hypoplastic left coronary cusp. Surgical repair was successful in both cases. Symptoms of myocardial ischemia in children with aortic valve disease should be investigated promptly to exclude obstruction of the coronary arteries.
与先天性主动脉瓣疾病相关的冠状动脉梗阻在儿童中很少见。我们研究了两名患有主动脉瓣疾病且有冠状动脉供血不足症状的儿童。电影血管造影显示左冠状动脉近端局限性梗阻。在一名患者中，一个膜样结构部分覆盖了主动脉瓣窦的左窦，几乎隔绝了左冠状动脉口；另一名患者左冠状动脉近端严重狭窄且先天性左冠状动脉瓣叶发育不全。两例手术修复均获成功。对于患有主动脉瓣疾病的儿童，应及时调查心肌缺血症状以排除冠状动脉梗阻。
