戈谢病的肾脏受累情况。
Renal involvement in Gaucher's disease.
作者信息
Siegal A, Gutman A, Shapiro M S, Griffel B
出版信息
Postgrad Med J. 1981 Jun;57(668):398-401. doi: 10.1136/pgmj.57.668.398.
Abstract
A patient with chronic Gaucher's disease is described who developed glomerulopathy 24 years after splenectomy terminating in renal failure. The pathological changes of this very rare complication of Gaucher's disease are described. The few similar cases reported in the literature are reviewed and the possible pathogenetic pathways discussed.
摘要
本文描述了一名慢性戈谢病患者，该患者在脾切除术后24年出现肾小球病变，最终发展为肾衰竭。文中描述了戈谢病这种极为罕见并发症的病理变化。回顾了文献中报道的少数类似病例，并讨论了可能的发病机制。
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