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将 Larsen 综合征与“先天性多发性关节挛缩症范畴”相区分。

Separating Larsen syndrome from the "arthrogryposis basket".

作者信息

Houston C S, Reed M H, Desautels J E

出版信息

J Can Assoc Radiol. 1981 Dec;32(4):206-14.

PMID:7328098
Abstract

Many patients with larsen syndrome have been misdiagnosed as having arthrogryposis. Larsen syndrome should be considered in any child with multiple joint dislocations, particularly when the knees are involved. Spinal malalignment of a serious degree was encountered in five of the six patients we report and appears to have been underemphasized previously. Two of the patients had unusual ossicles of uncertain derivation at the elbow. This has been described only five times before.

摘要

许多拉森综合征患者曾被误诊为关节挛缩症。对于任何有多关节脱位的儿童,尤其是膝关节受累时,都应考虑拉森综合征。我们报告的6例患者中有5例出现了严重程度的脊柱排列不齐,而这一点在之前似乎未得到足够重视。其中2例患者肘部有来源不明的异常小骨。此前仅有5次相关描述。

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