Lucci B, Zucco R
Riv Patol Nerv Ment. 1981 Jan-Feb;102(1):1-11.
Two cases of calcification of Striopallidodentate System will be considered. The first refers to a 20-years-old patient and features two small bilateral and symmetrical calcifications in the medial segment of globus pallidum. The first symptom, observed from the age 5 years was, behaviour disorder and, some years later, dystonia. The second case refers to a 54-years-old patient and features huge bilateral and symmetrical calcifications above and below the tentorium. The first symptoms started at the age of 32 with paraesthesiae and muscular contractions of the upper limbs, later with convulsive seizures and tetany and eventually right hemiplegia with aphasia. Study of Ca and P metabolism showed normoparathyroidism in the first case and idiopathic hypoparathyroidism in the second.
将考虑两例纹状体苍白球齿状系统钙化的病例。第一例涉及一名20岁的患者,其特征为苍白球内侧段有两个双侧对称的小钙化灶。从5岁起观察到的首个症状是行为障碍,几年后出现肌张力障碍。第二例涉及一名54岁的患者,其特征为小脑幕上下有巨大的双侧对称钙化灶。首个症状始于32岁,表现为上肢感觉异常和肌肉收缩,随后出现惊厥发作和手足搐搦,最终发展为右侧偏瘫伴失语。钙和磷代谢研究显示,第一例为甲状旁腺功能正常,第二例为特发性甲状旁腺功能减退。