Bofill D, Cabrer B, Grau A, Llebot J, Montis R, Vivancos J, Balcells A
Med Clin (Barc). 1980 Feb 10;74(3):104-6.
The authors report a case of hepatorenal polycystic disease discovered in the course of a routine physical examination. The patient was asymptomatic and the progression of the disease was extremely low. The existence of the disorder, however, was confirmed in the autopsy. Although hepatorenal polycystic disease is a relatively common clinical finding, the rareness of this condition in patients of advanced age and its occasionally asymptomatic form are pointed out. Clinical and prognostic characteristics of the two types of the disease (infantile and adult) are mentioned too. Physical examination and pyelography are the most import exploratory methods; other procedures such as echography, scanning and peritoneoscopy are complementary techniques. Lastly, the need to establish an early diagnosis in order to avoid unappropiated surgical maneuvers is stressed.
作者报告了一例在常规体检过程中发现的肝肾多囊性疾病病例。患者无症状,疾病进展极为缓慢。然而,该疾病的存在在尸检中得到了证实。虽然肝肾多囊性疾病是一种相对常见的临床发现,但指出了这种情况在老年患者中较为罕见,且偶尔呈无症状形式。还提到了该疾病两种类型(婴儿型和成人型)的临床及预后特征。体格检查和肾盂造影是最重要的检查方法;其他检查程序如超声检查、扫描和腹腔镜检查则是辅助技术。最后,强调了为避免不适当的手术操作而进行早期诊断的必要性。