Kamerling J P, Aarsen G J, Duran M, de Bree P K, van Sprang F J, Wadman S K
Clin Chim Acta. 1980 Mar 28;102(2-3):137-45. doi: 10.1016/0009-8981(80)90026-1.
The occurrence of gamma-glutamylphenylalanine in the urine of patients with phenylketonuria could be demonstrated using chromatographic techniques and mass spectrometry. Concentrations ranged up to 35 mg/l. Only a weak correlation between the urinary excretion of this compound and phenylalanine was seen. The ages of the patients investigated ranged from 2 weeks to 18 years. The origin of the dipeptide is discussed.
