Espana P, Figuera D, Fernandez de Miguel J M, Anaya A, Menendez J, Durantez A
Am J Gastroenterol. 1980 Jan;73(1):28-32.
Three cases of membranous obstruction of the inferior vena cava (IVC) are presented. Two of them underwent transcardiac membranotomy with good results. The third patient was treated symptomatically and died from gastrointestinal hemorrhage and hepatic coma two years after the diagnosis of Budd-Chiari syndrome. At autopsy, membranes were found in the inferior vena cava and hepatic veins. Differentiation of Budd-Chiari syndrome secondary to the presence of such a membrane is essential since these patients are potentially curable by surgical treatment. Cavography visualizes the obstruction and is the procedure of choice for diagnosis of this condition. Surgical treatment with transcardiac membranotomy is effective. Some hepatic abnormalities regress after surgery. Prophylactic postoperative treatment with diuretics seems advisable in these patients to prevent congestive cardiac failure.
本文报告了三例下腔静脉膜性梗阻病例。其中两例接受了经心膜切开术，效果良好。第三例患者接受了对症治疗，在被诊断为布加综合征两年后死于胃肠道出血和肝昏迷。尸检发现下腔静脉和肝静脉内有隔膜。区分继发于这种隔膜存在的布加综合征至关重要，因为这些患者有可能通过手术治疗治愈。腔静脉造影可显示梗阻情况，是诊断该病的首选检查方法。经心膜切开术的手术治疗是有效的。术后一些肝脏异常情况会有所改善。对这些患者术后预防性使用利尿剂似乎是可取的，以防止充血性心力衰竭。
