Finidori G, Rigault P, Barthel F, Mouterde P, Padovani J P
Chir Pediatr. 1978 Jul-Aug;19(4):211-7.
29 congenital radio-ulnar synostosis have been observed in 16 childrens. The authors review the clinical patterns of this affection: most often bilateral, it results in impossibility of pronosupination of the wrist which has but little functional consequence, if the hand is in an intermediary position. On the X-ray its almost always a superior radio-ulnar synostosis but the inferior radio-ulnar joint is abnormal and non functional. Only the children severely handicapped by a hand fixed in pronation should be operated upon. No good result can be hoped from a surgery that tries to restore pro-supination. The best surgical technique seems to be a simple horizontal osteotomy through the synostosis itself which allows a derotation of the forearm into the functional intermediary position. Severe complications can occur. Indications and technique must be very careful since this congenital abnormality is very well tolerated.
在16名儿童中观察到29例先天性桡尺骨融合。作者回顾了这种病症的临床模式：该病最常为双侧性，导致腕关节旋前旋后功能丧失，若手部处于中间位置，则功能影响较小。X线检查几乎总是显示上桡尺关节融合，但下桡尺关节异常且无功能。只有因手部固定于旋前位而严重致残的儿童才应接受手术。试图恢复旋前旋后功能的手术不会取得良好效果。最佳手术技术似乎是通过融合部位进行简单的水平截骨，使前臂旋转至功能中间位。可能会发生严重并发症。由于这种先天性异常耐受性良好，手术指征和技术必须非常谨慎。
