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引用本文的文献
1
Apparently normal extracellular acidic alpha-mannosidase in fibroblast cultures from patients with mannosidosis.
Am J Hum Genet. 1982 Jan;34(1):100-11.
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1
Protein measurement with the Folin phenol reagent.
J Biol Chem. 1951 Nov;193(1):265-75.
2
Evidence for a non-lysosomal alpha-mannosidase in rat liver homogenates.
Biochim Biophys Acta. 1971 Apr 14;235(1):142-8. doi: 10.1016/0005-2744(71)90041-6.
3
Human mannosidosis--the enzyme defect.
Biochem Biophys Res Commun. 1972 Oct 17;49(2):579-83. doi: 10.1016/0006-291x(72)90450-0.
4
A recognition marker required for uptake of a lysosomal enzyme by cultured fibroblasts.
Biochem Biophys Res Commun. 1974 Mar 15;57(1):55-61. doi: 10.1016/s0006-291x(74)80356-6.
5
A hypothesis for I-cell disease: defective hydrolases that do not enter lysosomes.
Biochem Biophys Res Commun. 1972 Nov 15;49(4):992-9. doi: 10.1016/0006-291x(72)90310-5.
6
Multiple lysosomal enzyme deficiency due to enzyme leakage?
N Engl J Med. 1971 Jan 14;284(2):109-10. doi: 10.1056/NEJM197101142840221.
7
Activation by ferrous ions of an alpha-mannosidase in rat testis and liver.
Biochem Soc Trans. 1973 Nov;1(6):1266-7. doi: 10.1042/bst0011266.
8
Mannosidosis in Angus cattle. The enzymic defect.
Biochem J. 1974 Feb;137(2):363-71. doi: 10.1042/bj1370363.
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Residual altered alpha-mannosidase in human mannosidosis.
Biochem Biophys Res Commun. 1976 Jan 12;68(1):292-8. doi: 10.1016/0006-291x(76)90042-5.
10
Cellular transport of lysosomal enzymes: an alternative hypothesis.
Biochem J. 1977 Apr 15;164(1):281-2. doi: 10.1042/bj1640281.
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