胱氨酸尿症的谷氨酰胺治疗

Glutamine therapy of cystinuria.

作者信息

Van Den Berg C J, Jones J D, Wilson D M, Smith L

出版信息

Invest Urol. 1980 Sep;18(2):155-7. doi: 10.1007/978-1-4684-8977-4_26.

Abstract

We studied the urinary excretion of cystine, acids, and cystine crystalluria in five patients with homozygous cystinuraia before and during oral glutamine therapy. Oral glutamine did not change the absolute urinary excretion or fractional excretion of cystine in our patients and did not significantly affect urinary pH. Cystine crystalluria was present before and during oral glutamine therapy.

摘要

我们研究了5例纯合子胱氨酸尿症患者在口服谷氨酰胺治疗前后的胱氨酸尿排泄、酸排泄及胱氨酸结晶尿情况。口服谷氨酰胺并未改变我们患者的胱氨酸绝对尿排泄量或分数排泄量，且对尿液pH值无显著影响。在口服谷氨酰胺治疗前后均存在胱氨酸结晶尿。