Rondot P, de Recondo J, Benhamou C L, Sicard D, Daumas-Duport C
Ann Med Interne (Paris). 1980;131(4):203-8.
Three cases of cerebral vascularitis are reported. This affection does not occur frequently and is often unrecognized. It can be isolated or associated with disease such as sarcoidosis, Behcet's disease, or collagen disorders (lupus erythematosus, mixed connective tissue diseases). Diagnosis is made from the evolution with transient remission, the inflammatory nature of the CSF, and the presence of segmentary narrowing on arteriography. In case of doubt an exploratory operation with biopsy is necessary. The most likely etiology is an auto-immune disturbance, and cortico-therapy has greatly improved the prognosis.
报告了3例脑血管炎病例。这种疾病并不常见,且常常未被识别。它可以是孤立的,也可与结节病、白塞病或胶原病(红斑狼疮、混合性结缔组织病)等疾病相关。根据病情有短暂缓解、脑脊液的炎性性质以及血管造影显示节段性狭窄来做出诊断。如有疑问,需进行活检的探查手术。最可能的病因是自身免疫紊乱,皮质激素治疗已大大改善了预后。