Webster J R, Battifora H, Furey C, Harrison R A, Shapiro B
Am J Med. 1980 Nov;69(5):786-9. doi: 10.1016/0002-9343(80)90453-2.
A brother and sister with classic, biopsy proved pulmonary alveolar proteinosis are described. Both had low serum and low normal secretory immunoglobulin A (IgA) levels. A tendency for familial occurrence is possible and it is recommended that patients with pulmonary alveolar proteinosis, and their families, be evaluated for immunologic deficiencies.
本文描述了一对经活检证实患有典型肺泡蛋白沉积症的兄妹。他们的血清分泌型免疫球蛋白A(IgA)水平均较低且处于正常低限。肺泡蛋白沉积症可能存在家族发病倾向,建议对肺泡蛋白沉积症患者及其家属进行免疫缺陷评估。