Riedel H
Zentralbl Allg Pathol. 1980;124(5):410-5.
Report of necropsy findings of a 17 years old girl with a progeria syndrome. There was a high degree of generalized atherosclerosis, involving the visceral arteries, chiefly those to the kidneys. The patient died of nephrosclerosis with uraemia. The aetiology of progeria syndrome remains obscure, single findings (lipoprotein- and amino-acid metabolism) may be understood as an inborn error of metabolism.
一名患有早衰综合征的17岁女孩的尸检结果报告。存在高度的全身性动脉粥样硬化,累及内脏动脉,主要是肾动脉。患者死于肾硬化伴尿毒症。早衰综合征的病因仍不清楚,单一的发现(脂蛋白和氨基酸代谢)可被理解为一种先天性代谢缺陷。