Kaul U, Arora R, Rani S
Am Heart J. 1980 Nov;100(5):673-7. doi: 10.1016/0002-8703(80)90234-3.
An acyanotic 4-year-old male child who failed to thrive presented with signs of persistent right heart failure and no cardiac murmurs. There was radiologic evidence of gross cardiomegaly with unremarkable lung fields. Cardiac catheterization and cineangiographic features helped in arriving at the diagnosis of parchment right ventricle with normal tricuspid valve (Uhl's anomaly), a rare condition seldom diagnosed during life. The patient was subjected to surgery, and Glenn's operation was performed, following which he died of a low output state and bradyarrhythmia. Autopsy revealed partial parchment right ventricle with rudimentary pulmonary valve leaflets, a combination not described previously.
一名4岁发育不良的无紫绀男童，出现持续性右心衰竭体征且无心脏杂音。放射学证据显示心脏明显增大，肺野无异常。心导管检查和心血管造影特征有助于诊断为三尖瓣正常的羊皮纸样右心室（乌尔畸形），这是一种罕见疾病，生前很少被诊断出来。该患者接受了手术，进行了格林手术，术后死于低心排血量状态和缓慢性心律失常。尸检发现部分羊皮纸样右心室伴有发育不全的肺动脉瓣叶，这种组合此前未曾有过描述。
