Canty T G
J Thorac Cardiovasc Surg. 1981 Jan;81(1):96-9.
A 17-day-old infant with a right-sided extralobar pulmonary sequestration associated with an intact diaphragmatic hernia sac presented as an acute respiratory emergency. The diagnosis was obscured by the initial resuscitative treatment of cardiorespiratory arrest necessitating positive-pressure ventilation complicated by bilateral tension pneumothoraces prior to transfer. At operation, unique systemic arterial and venous communications to the sequestration from the dome of the liver through the intact hernia sac were found. A bronchial communication to the right main bronchus was also present. Histologic examination of the sequestration specimen revealed other features common to both intralobar and extralobar sequestration. This case lends support to the hypothesis of a common embryologic basis for both types of sequestration, as well as other congenital pulmonary cystic abnormalities, and the association with diaphragmatic hernia.
一名17天大的婴儿，患有右侧肺叶外隔离症，伴有完整的膈疝囊，表现为急性呼吸急症。在转运前，心肺骤停的初始复苏治疗因双侧张力性气胸而需要进行正压通气，这使得诊断变得模糊不清。手术中发现，有独特的体循环动静脉通过完整的疝囊与来自肝穹窿的隔离肺相通。还存在一条与右主支气管相通的支气管。对隔离肺标本的组织学检查显示了叶内型和叶外型隔离症的其他共同特征。该病例支持了两种类型的隔离症以及其他先天性肺囊性异常具有共同胚胎学基础的假说，以及与膈疝的关联。
